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N-Carbamyl-L-glutamic acid

 - Carglumic acid  - Carbamylglutamate
Axon 3816
CAS:  1188-38-1
  • Optical Purity:  Optically pure
  • Soluble in water, 0.1N NaOH(aq), DMSO and EtOH
  • MF:  C6H10N2O5
  • MW:  190.15

Description

N-Carbamyl-L-glutamic acid, a deacylase-resistant analogue of N-acetylglutamate, is a carbamyl phosphate synthetase 1 (CPS1) activator. N-Carbamyl-L-glutamic acid is used to treat primary N-acetyl-L-glutamate synthase deficiency and hyperammonemia associated with organic acidemias such as methylmalonic aciduria, propionic aciduria, and isovaleric aciduria.

More Information

Parent CAS No. 1188-38-1
Chemical Name (S)-2-Ureidopentanedioic acid
SMILES C(=O)(N)N[C@H](C(O)=O)CCC(=O)O |&1:4,r|
MFCD N.A.
InChi InChI=1S/C6H10N2O5/c7-6(13)8-3(5(11)12)1-2-4(9)10/h3H,1-2H2,(H,9,10)(H,11,12)(H3,7,8,13)/t3-/m0/s1
InChiKey LCQLHJZYVOQKHU-VKHMYHEASA-N
CID 121396
Short Description CPS1 activator
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